Investigation of Poor Academic Achievement in Children with Duchenne Muscular Dystrophy

Duchenne Muscular Dystrophy (DMD) is a neurogenetic developmental disorder that presents with progressive muscular weakness. It is caused by a mutation in a gene that results in the absence of specific products that normally localize to muscle cells and the central nervous system (CNS). The majority of affected individuals have IQs within the normal range, generally with lower verbal than performance IQ scores. Prior work has demonstrated selective deficits on tests of verbal span and immediate memory. For the current study, 26 boys with DMD (and normal intellectual function) and their unaffected siblings were evaluated. Paired comparisons demonstrated that the children with DMD had significantly poorer academic achievement scores than their siblings, even though their vocabulary levels and home and educational environments were comparable. Children with DMD also had more behavioral concerns, physical disabilities, and poorer verbal memory spans. Linear regression indicated that behavioral concerns, executive function, and physical disability did not contribute substantially to academic performance, whereas performance on verbal span did. DMD presents with a selective developmental aberration in verbal span that has wide‐ranging consequences on learning skills.     

The turning point in 1985. The history of appraisal and disposal of records in Iceland

The article sets off with a brief summary of the history of appraisal and disposal of records as processed at the National Archives of Iceland (NAI) since its establishment in 1882 to present times. Rules on appraisal and disposal of records introduced in 1900, 1911, and 1916 were ignored and all records were kept. Status quo remained until 1985 when a new National Archives Act was passed. The appraisal and disposal process adopted then is described and explained. It included the publication of instructions on records management as well as forms relating to records management. The influence of acts of law on the appraisal and disposal process is explained. Finally the experience with the arrangement of organised appraisal in Iceland is described.     

Metaphor and Totem: Exploring and evaluating prior experiential learning

The evaluation and recognition of prior experiential learning is now well established. A significant issue in such evaluations has been the centrality of the learner and his/her empowerment in the educational process. However, most models of evaluation require equivalency between the unique experiences of the subject and existing course analogues. In these models evaluation is based on metaphor, on finding varying degrees of similarity between the experience being assessed and currently existing academic structures. The present paper calls for a richer perspective to be taken in assessing prior experiential learning with particular interest being seen in the notion of totemism as characterised by anthropologist Claude Levi-Strauss. A replacement of metaphor by totemism may restore power, ownership and centrality of the experience to the candidate for assessment, while allowing evaluators an opportunity to engage in a novel but authentic articulation of the underlying academic equivalency of the experience.     

Interlibrary loan and commercial document supply: Finding the right fit

This study examined the cost and performance of six commercial document suppliers accessible via OCLC, and comapared their service to that of traditional interlibrary loan (ILL). Results indicated that, while commercial firms cannot be recommended as a wholesale replacement for ILL, they can add much-needed flexibility to a library's overall plan for document delivery.