Investigation of Poor Academic Achievement in Children with Duchenne Muscular Dystrophy

Duchenne Muscular Dystrophy (DMD) is a neurogenetic developmental disorder that presents with progressive muscular weakness. It is caused by a mutation in a gene that results in the absence of specific products that normally localize to muscle cells and the central nervous system (CNS). The majority of affected individuals have IQs within the normal range, generally with lower verbal than performance IQ scores. Prior work has demonstrated selective deficits on tests of verbal span and immediate memory. For the current study, 26 boys with DMD (and normal intellectual function) and their unaffected siblings were evaluated. Paired comparisons demonstrated that the children with DMD had significantly poorer academic achievement scores than their siblings, even though their vocabulary levels and home and educational environments were comparable. Children with DMD also had more behavioral concerns, physical disabilities, and poorer verbal memory spans. Linear regression indicated that behavioral concerns, executive function, and physical disability did not contribute substantially to academic performance, whereas performance on verbal span did. DMD presents with a selective developmental aberration in verbal span that has wide‐ranging consequences on learning skills.     

Reconceptualising educational assessment in South Africa — testing times for teachers

This paper explores some of the problems arising when Continuous Assessment (CA) is grafted onto established pedagogic practices. It focuses on three issues: teachers' restricted understandings of assessment, teachers' emphasis on criteria that demonstrate concern with social control, and some of the problems connected with peer assessment. Two vignettes derived from fieldwork associated with a project to improve the quality of primary education are used to raise the issues. We argue that the development of desired practices is hampered above all by tacit values in tension with those underpinning the new curriculum. These values, together with the complexity of curriculum design, create serious problems of manageability and interpretation, which can only be addressed through detailed interactive in-service training, aimed at reconceptualising teachers' notions of assessment.     

Copyright complicance in the electronic age: Conceptual issues

This article focuses on several conceptual and structural issues that are central to copyright compliance in the electronic age. It presumes the development of a national electronic network for storing, organizing, accessing, managing, and charging for information. The article first discusses the implications of constructing a comprehensive electronic “highway,” or Digital Library System (DLS), which would link information to the widespread community of users. It then presents the ramifications of a highly decentralized set of subsystems serving rights holders and users, linked by protocols established by the DLS. A discussion of the implications of digital interchangeability for copyright follows. The article ends with an analysis of alternatives to existing intellectual property rights conveyance systems, and concludes that current ownership structures, and systems for conveying rights and royalties, will remain the foundation for copyright in the electronic world. This article appeared in a slightly different form in theProceedings of the Twelfth National Online Meeting—1991, and is published here with the permission of Learned Information, Inc., Medford, N.J.