Maple syrup urine disease: An uncommon cause for neonatal metabolic distress

Maple Syrup Urine Disease is an autosomal recessive disorder caused by a deficiency in the activity of the branched-chain α-ketoacid dehydrogenase complex. This rare disorder represents one of the causes of acute neonatal illness which results in devastating disturbances of neurological development. On investigation of 1750 infants with neurological impairment for inborn errors of amino acid metabolism, 4 neonates with classical maple syrup urine disease were detected. These otherwise normal neonates presented in the first week after birth with seizures, lethargy and refusal of feeds, hypoglycemia and metabolic acidosis. The plasma and urine concentrations of the branched-chain amino acids were increased and there was ketoaciduria. Two of these neonates expired before specific treatment could be instituted. Routine biochemical screening of neonates with acute illness could unearth many cases of this rare inherited metabolic disease.     

Trends in Instructional Design: Emerging Theory-Based Models

Currently, instructional design theorists are generating new enhancements of traditional design models on both macro and micro levels. This paper summarizes the anticipated changes in instructional design models that will result from today's theoretical activity. It addresses issues such as linearity in the design process, enhanced roles of analysis and evaluation, and the new emphasis on learner control and transfer of training. These model enhancements are being influenced by new interpretations of general systems theory and cognitive learning theory, constructivism, chaos theory, and situated cognition. Predicted model changes also reflect the impact of the new technologies, designer decision-making research, and the performance technology and total quality management movements. These and other intellectual forces are likely to produce diverse models for future designers.     

The relationship of ethnic identity and ego identity status among adolescents and young adults

A multi-ethnic sample of 248, ages 13–26, was used to examine the effects of age, gender, and ethnic group membership on ethnic identity and ego identity scores. Subjects were recruited from college and public schools in a large northeastern metropolitan area. The multigroup ethnic identity measure (MEIM) was used to assess ethnic identity and ego identity status was measured by the extended objective measure of ego identity status (EOMEIS). An age by ethnic group design was employed. Consistent findings of significant ethnic group differences in levels of ethnic identity were observed. Age and ethnic group were found to contribute differently to ethnic identity and ego identity status. The relationship between ethnic identity and ego identity status was found to be pronounced among subjects of color but not as dramatic as hypothesized.     

Muscle Dysmorphia Among College Men: An Emerging Gender‐Related Counseling Concern

Recent literature suggests that, like midrange eating disorders among college women, male muscle dysmorphia is emerging as a physical as well as a health concern among college men. The authors define the disorder, review diagnostic and etiological considerations, and discuss the added complication of creatine use to self‐manage muscle dysmorphic symptoms. Implications for the college counseling practice are presented, and the need for a reliable knowledge base to guide practice is emphasized.     

Comparison of 1 and 2 days per week of strength training in children

The purpose of this study was to compare the effects of 1 and 2 days per week of strength training on upper body strength, lower body strength, and motor performance ability in children. Twenty-one girls and 34 boys between the ages of 7.1 and 12.3 years volunteered to participate in this study. Participants strength trained either once per week (n = 22) or twice per week (n = 20) for 8 weeks at a community-based youth fitness center. Each training session consisted of a single set of 10-15 repetitions on 12 exercises using child-size weight machines. Thirteen children who did not strength train served as age-matched controls. One repetition maximum (1RM) strength on the chest press and leg press, handgrip strength, long jump, vertical jump, and flexibility were assessed at baseline and posttraining. Only participants who strength trained twice per week made significantly greater gains in 1RM chest press strength, compared to the control group (11.5 and 4.4% respectively, p < .05). Participants who trained once and twice per week made gains in 1RM leg press strength (14.2 and 24.7%, respectively) that were significantly greater than control group gains (2.4%). On average, participants who strength trained once per week achieved 67% of the 1RM strength gains. No significant differences between groups were observed on other outcome measures. These findings support the concept that muscular strength can be improved during the childhood years and favor a training frequency of twice per week for children participating in an introductory strength training program.