Organic Acidurias: An Updated Review

Organic acidurias are an important class of inherited metabolic disorders arising due to defect in intermediary metabolic pathways of carbohydrate, amino acids and fatty acid oxidation. This review summarizes the current knowledge about the important organic acidurias in the Indian population. Specifically, diagnosis and principles of treatment of organic acidurias are covered. The salient features of common organic acidurias as well as their prevalence in various parts of the world are reviewed in some detail.     

基于知识吸收与创造的市场导向和组织创新关系研究

在文献回顾的基础上,提出市场导向促进组织创新机制研究的假设模型,并通过对长三角地区463家企业的问卷调查对这一模型进行了验证。研究认为,市场导向可以分为信息获取、信息传播、市场反应等三个方面。信息获取对组织创新没有直接显著影响;信息传播既对组织创新产生直接影响,又通过知识吸收与创造对组织创新产生间接影响;市场反应既对组织创新产生直接影响,又通过知识吸收与创造对组织创新产生间接影响。     

三维Q值层析成像人机交互软件及其在地震数据处理中的应用

Q值结构对了解地壳的非弹性性质、地壳内部构造、热活动状态、地壳介质非均匀性以及断层分布有着重要的意义.编写了基于吸收特征时间t*的三维Q值层析成像人机交互软件,可以方便快捷地计算地震体波（P波和S波）的振幅谱并通过拟合振幅谱得到反映地震波衰减的吸收特征时间t*,并利用t*资料通过三维Q值层析成像方法得到三维Q值结构.实际观测资料处理结果表明,文中给出的方法和软件是有效且可行的.     

电感耦合等离子体原子发射光谱法同时测定长石中七种常见元素

采用氢氟酸-硝酸-高氯酸溶解试样,电感耦合等离子体原子发射光谱法测定长石中铝、钙、铁、钾、镁、钠、钛等七种常见元素,探讨了元素的分析谱线、试样的溶解体系对测定的影响。通过对方法标准工作曲线、检出限o．59～3．76μg／L、相对标准偏差（RSD,n=9）0．3～9．3％、标准误差（KE）-6．67~10．53％的试验,经长石国家标准物质验证和方法对照,测定值与认定值无明显差异。方法简单、快速、准确,可满足长石中相关元素的测定。     

Aroma changes of black tea prepared from methyl jasmonate treated tea plants

研究目的：为茉莉酸甲酯诱导来提高茶叶香气品质提供理论依据,为新型花香红茶的研制提供技术支持。创新要点：首次将茉莉酸甲酯应用于诱导茶叶香气品质提高,初步验证了茶叶香气品质提高的本质原因：相关酶活性提高,基因表达上调。研究方法：采用顶空固相微萃取法（HS-SPME）对红茶香气进行富集,气相色谱-质谱联用仪（GC-MS）进行解吸附分析,实时定量多聚酶链式反应（qRT-PCR）分析茶鲜叶中香气相关酶基因表达。重要结论：茉莉酸甲酯诱导后的茶鲜叶中多酚氧化酶（PPO）活性上升,β-葡萄糖苷酶活性下降;PPO和β-樱草糖苷酶基因表达上调,β-葡萄糖苷酶基因表达下调。茉莉酸甲酯诱导后的茶鲜叶能明显提高由其制成的红茶香气品质,且萜烯醇类和萜烯类含量明显提高。     

生物组织光学特性参数测量原理及设计

从光的传输理论出发，利用漫射近似方程，推导出当无限细脉冲光及连续光束垂直入射到生物组织表面时，生物组织表面漫反射光随空间及时间变化的解析表达式，由此表达式出发，设计了一套实验装置，分析了生物组织光学特性参数的测量方法，以及如何对实验数据进行处理。     

地表水和海水中微量砷、汞的联合测定法

应用AFS-2202a型原子荧光光度计对地表水和海水中的砷、汞联合测定方法进行有苴的研究。通过实验，探讨总结出了合理有效的水样前处理方法和实用测定步骤。并对其最低检出下限、精密度和准确度进行了全面评估，结果表明：该方法具有操作简便、快速、干扰少、灵敏度高等优点，适用于地表水和海水中微量砷、汞元素的联合测定，具有很好的可行性和适用性。     

原子物理教学与创新精神的培养

分析了原子物理学在物理学中的地位,指出原子物理学课程含有丰富的物理方法,提出原子物理学教学可培养学生的创新精神。     

基于阐释翻译理论的翻译实践方法研究

对阐释翻译理论概念起源和发展历程进行了深入研究。结合翻译的实际操作过程从阐释学的四个基本步骤：信任、入侵、吸收和补偿。分别进行了详细的解释和论述,深入研究了给予阐释学理论在翻译实践的具体操作过程。之后重点从翻译过程中文化背景的转换、表达方式的转换、意境的重构等方面给出了阐释学的翻译应用实践方法。     

Nineteenth century chrome yellow and chrome deep from Winsor & NewtonTM

The Winsor & Newton^TM (W&N) nineteenth century archive database includes digitised images of hand-written instructions and workshop notes for the manufacture of their artists’ materials. For the first time, all 183 production records for yellow lead chromate pigments were studied and evaluated. They revealed that W&N produced essentially three pigment types: lemon/pale based on mixed crystals of lead chromate and lead sulphate [Pb(Cr,S)O₄]; middle on pure monoclinic lead chromate [PbCrO₄]; and deep that contains the latter admixed with basic lead chromate [Pb₂CrO₅]; accounting for 53, 22, and 21% of the production, respectively. Production records for primrose (4%) were also included since the formulation results in mixed crystals with a high percentage of lead sulphate, which, according to the literature, leaves it more prone to degradation. Each pigment type is characterised by only one or two main synthetic pathways; process variations reveal a systematic and thorough search for a high-quality durable product. A comparison of the chemical composition of pigment reconstructions with early W&N oil paint tubes showed that their records entitled ‘pale’ and ‘lemon’ correlated with the pigment in their tube labelled chrome yellow and, ‘middle’ and ‘deep’ with the label chrome deep. Lemon and middle pigment formulations were made into oil paints to assess their relative photo-stability. The degradation process was followed by colorimetry and was studied by synchrotron radiation-based techniques. Based on the X-ray absorption spectroscopy data, the possibility for creating a stability index for chrome yellows is discussed.