CANDU6核电厂失去凝结水故障预想及诊断

CANDU6机组曾多次发生过失去凝结水导致的瞬态,有的甚至造成停机停堆。为了探讨运行人员对凝结水系统故障诊断的方向,本文通过介绍凝结水系统的特点,对失去凝结水的故障进行了事故预想,并提出了处理要点。另外,本文还对失去凝结水对电厂的影响做了简要的分析。     

Two unrelated patients with rare Crigler-Najjar syndrome type I: two novel mutations and a patient with loss of heterozygosity of UGT1A1 gene

Crigler-Najjar syndrome type I (CN-I) is the most severe type of hereditary unconjugated hyperbilirubinemia. It is caused by homozygous or compound heterozygous mutations of the UDP-glycuronosyltransferase gene (UGT1A1) on chromosome 2q37. Two patients clinically diagnosed with CN-I were examined in this paper. We sequenced five exons and their flanking sequences, specifically the promoter region of UGT1A1, of the two patients and their parents. Quantitative real-time polymerase chain reaction (qRT-PCR) was used to determine the UGT1A1 gene copy number of one patient. In patient A, two mutations, c.239_245delCTGTGCC (p.Pro80HisfsX6; had not been reported previously) and c.1156G>T (p.Val386Phe), were identified. In patient B, we found that this patient had lost heterozygosity of the UGT1A1 gene by inheriting a deletion of one allele, and had a novel mutation c.1253delT (p.Met418ArgfsX5) in the other allele. In summary, we detected three UGT1A1 mutations in two CN-I patients: c.239_245delCTGTGCC (p.Pro80HisfsX6), c.1253delT (p.Met418ArgfsX5), and c.1156G>T (p.Val386Phe). The former two mutations are pathogenic; however, the pathogenic mechanism of c.1156G>T (p.Val386Phe) is unknown.     

对民事审判中合同纠纷案件损失数额认定的思考——以经验法则为视角

在民事审判中合同纠纷案件损失数额的认定是一个绕不开的问题,达到＂客观真实＂是一个努力争取的目标;当不能达到＂客观真实＂目标时,根据经验法则及相关规定,只要达到了＂高度盖然性＂的标准也同样达到了各方面所要求的证明标准,这才是合同纠纷案件中损失数额认定的＂应然＂状态。要改变合同纠纷案件中损失数额认定的混乱状态,有赖于各方的努力。     

歌剧《盼你归来》的视觉呈现

分析歌剧《盼你归来》的舞台设计、舞美元素、灯光设计及视觉呈现。     

一种固态聚合物损耗因子测试方法实验研究

宽频带随机振动冲击噪声会激发结构许多谐振峰,利用粘弹阻尼技术隔振、减振和降噪是一项新的技术措施,尤其是对于宽带随机振动和噪声控制具有特殊效果。在实际减振、降噪工程设计中往往需要知道所选用材料的损耗因子,复模量E*的温度谱的测量已经有专门的论述和成熟的方法。根据一个具体的实验研究探讨频率域复模量的测量进而计算材料的损耗因子。     

从田园耕作到别业樵歌——论孟浩然对陶潜田园诗文化内涵的继承与衍变

孟浩然由于其独特的人生经历 ,继承了陶诗返朴归真的文化内涵 ,但同时其诗在田园主题、田园景色的实质及创作手法等方面又表现出明显的差异 ,呈现了田园诗模式的时代转换。这种转换意味着山水田园之美与个性自由、风流洒脱的盛唐文化精神趋向有机统一     

连续随机变量的随机独立与回归独立性的关系

回归独立性是指给定随机变量X是随机变量Y的条件期望E（Y｜X）不依赖于X，前人讨论了离散型随机变量回归独立性的关系，得到了二者等价的充分必要条件。对连续型随机变量的情况加以讨论，获得了二者等价的几个充分必要条件，并说明在统计分析中的应用。     

科技创新团队基于机会损失的绩效测量原理与方法

科技创新团队经常使用目标与业绩之间差异等单一测度方法进行绩效评价往往存在一些问题，因为制定目标时所使用的基本条件在目标实施时往往会发生变化，制定目标值时存在的一些偏见可能促使部分目标值优化。为了更好地测量科技创新团队绩效，提出基于实际值对比基准值得到的实际条件下基于最佳运营行动得到的利润与最佳利润的差异，即基于机会损失评价科技创新团队绩效的方法。研究表明：基于机会损失测量科技创新团队绩效需要运用整体最佳利润和部分最佳利润、总利润和整体机会损失及部分机会损失的原理与方法；此外，复数科技创新团队的情况下需要考虑两部分最佳利润，此时会发生4种部分机会损失。进一步探讨和说明两个科技创新团队基于机会损失的科技创新团队绩效测量原理与方法。     

The private returns to education in rural Bangladesh

This study estimates the private average rate of return (ARR) and internal rate of return (IRR) to education in rural Bangladesh. Using data from the Bangladesh Integrated Household Survey (BIHS) 2015, we estimate average returns using the Mincerian method and IRR using the full method, accounting for both the direct and indirect costs of schooling. To account for endogeneity and selection bias, we use parental education as an instrumental variable and apply the Heckman correction method. We find an average return of 18 %, an IRR of 12 % for tertiary education, 4.86 % for secondary, and 5.24 % for primary. In the agricultural sector specifically, however, returns to tertiary education are more in line with primary and secondary education.     

略论"回归生活"与高校道德教育

针对当前高校道德教育脱离实际道德生活的状况,分析了"回归生活"的道德教育的内涵、特征,并提出了道德教育回归生活世界的实践途径.